Type I
form of severe, affects 43% of patients and is autosomal dominant.
In this way, the clinical symptoms are usually severe.
Patients who have marked a section of skin wounds and scars frequently in various parts of the body.
Surgical sutures heal properly, with a slight dehiscence.
Hypermobility is very strong and affects all parts of the body.
Spontaneous fractures may occur, but an immediate reduction is simple.
Varicose veins and pseudotumors Molluscoida are frequent.
Musculo-skeletal features are easy to find. These features include kyphoscoliosis) Hallus valgus flat foot (eg flat feet and genu recurvatum; contusions are less common in this type than in other forms.
Heart disease, especially heart mitral valve prolapse, are sometimes available.
With a premature rupture of fetal membranes is specific for that type.
Type II are the Mitis, affects 35% of patients and is autosomal dominant.
This group is characterized by a soft light of the functions of type I.
Large scars are often, but the skin has a slightly lower sensitivity and bruisability.
The joints are moderately hyperextensible, and the figures are usually only interested in the body.
Type III the benign hypermobile familial form, affects 10% of patients and is autosomal dominant.
Patients with this variant have no or only minimal changes in the skin, but have a hypermobility affects multiple joints.
This usually results hyperextensibility orthopedic consequences (eg severe osteoarthritis) in the long term.
Type IV which bruises and blood pressure affects 6% of patients and is an autosomal recessive or, sometimes as an autosomal dominant.
This variant is relatively rare.
Clinically, the patients were single, white, translucent skin and the underlying vessels are easily recognizable.
The skin is sensitive, but not expandable.
Molluscoida pseudotumors are many scars and bruises, and hemorrhagic lesions.
Scars and hyperpigmentation are common.
Common Hyperextensibility is rare or absent.
Arterial aneurysms, mitral valve and spontaneous pneumothorax are frequent complications.
Patients also have a low weight and small size.
The prognosis of this type is poor, and the patient \ 's life is shortened.
Sudden death can occur after a visceral perforation or after the collapse of a large vessel, usually a stomach or a ship of the spleen.
Prenatal diagnosis by restriction of polymorphic DNA analysis is possible.
Type V, the X-linked form, affects 5% of patients and is X-linked recessive.
Skin of patients with this form of Ehlers-Danlos syndrome is very elastic and orthopedic frequent.
Bruising and laxity are rare.
Type VI the ocular form, the disease affects about 2% of patients and is an autosomal recessive trait.
Patients of this type are clinically severely affected by the disease.
Unable to perform Translation:invalid result dataPatients may have multiple scars, some of which are hyperpigmented.
Joints are hyperextensible.
This subgroup has eyes only of clinical symptoms. The fragile eye can cause bleeding and retinal detachment, glaucoma and color of the sclera. Outside the world is rare, but possible.
The action of LH in the amniotic fluid can be used to predict the outcome of pregnancy.
Type VII or more arthrochalasis congenita, affects 3% of patients and is an autosomal recessive or autosomal dominant.
Patients with this type of significant hyperextensibility common, but the lesions are less severe than those of other species.
Patients spontaneous dislocation, often with a rapid reduction.
Patients of this type are generally small.
Type VII the form periodontitis is rare and is inherited as an autosomal dominant.
Patients of this type have a dental examination with periodontal gum.
Sagging skin, joint and hyperextensibility bruisability vary.
Gingival resorption and loss of permanent teeth when the patient at the age of 30 years is common.
IX or X-linked cutis laxa type is rare, and a structure in X-linked recessive.
Patients with type IX bilateral bony features on the back.
Rarely the skin and joints are affected.
Chronic diarrhea and outcome of orthostatic hypotension are unique in this group.
The scars are usually visible, because the treatment is poor.
Patients of this type have a defect in intracellular copper-dependent enzymes, similar to that of patients with Menkes syndrome.
Type X (fibronectin deficiency) and type XI (benign hypermobility syndrome) is a rare form of Ehlers-Danlos syndrome. Some suggest that these species are so similar that you are better classified as a category 2
form of severe, affects 43% of patients and is autosomal dominant.
In this way, the clinical symptoms are usually severe.
Patients who have marked a section of skin wounds and scars frequently in various parts of the body.
Surgical sutures heal properly, with a slight dehiscence.
Hypermobility is very strong and affects all parts of the body.
Spontaneous fractures may occur, but an immediate reduction is simple.
Varicose veins and pseudotumors Molluscoida are frequent.
Musculo-skeletal features are easy to find. These features include kyphoscoliosis) Hallus valgus flat foot (eg flat feet and genu recurvatum; contusions are less common in this type than in other forms.
Heart disease, especially heart mitral valve prolapse, are sometimes available.
With a premature rupture of fetal membranes is specific for that type.
Type II are the Mitis, affects 35% of patients and is autosomal dominant.
This group is characterized by a soft light of the functions of type I.
Large scars are often, but the skin has a slightly lower sensitivity and bruisability.
The joints are moderately hyperextensible, and the figures are usually only interested in the body.
Type III the benign hypermobile familial form, affects 10% of patients and is autosomal dominant.
Patients with this variant have no or only minimal changes in the skin, but have a hypermobility affects multiple joints.
This usually results hyperextensibility orthopedic consequences (eg severe osteoarthritis) in the long term.
Type IV which bruises and blood pressure affects 6% of patients and is an autosomal recessive or, sometimes as an autosomal dominant.
This variant is relatively rare.
Clinically, the patients were single, white, translucent skin and the underlying vessels are easily recognizable.
The skin is sensitive, but not expandable.
Molluscoida pseudotumors are many scars and bruises, and hemorrhagic lesions.
Scars and hyperpigmentation are common.
Common Hyperextensibility is rare or absent.
Arterial aneurysms, mitral valve and spontaneous pneumothorax are frequent complications.
Patients also have a low weight and small size.
The prognosis of this type is poor, and the patient \ 's life is shortened.
Sudden death can occur after a visceral perforation or after the collapse of a large vessel, usually a stomach or a ship of the spleen.
Prenatal diagnosis by restriction of polymorphic DNA analysis is possible.
Type V, the X-linked form, affects 5% of patients and is X-linked recessive.
Skin of patients with this form of Ehlers-Danlos syndrome is very elastic and orthopedic frequent.
Bruising and laxity are rare.
Type VI the ocular form, the disease affects about 2% of patients and is an autosomal recessive trait.
Patients of this type are clinically severely affected by the disease.
Unable to perform Translation:invalid result dataPatients may have multiple scars, some of which are hyperpigmented.
Joints are hyperextensible.
This subgroup has eyes only of clinical symptoms. The fragile eye can cause bleeding and retinal detachment, glaucoma and color of the sclera. Outside the world is rare, but possible.
The action of LH in the amniotic fluid can be used to predict the outcome of pregnancy.
Type VII or more arthrochalasis congenita, affects 3% of patients and is an autosomal recessive or autosomal dominant.
Patients with this type of significant hyperextensibility common, but the lesions are less severe than those of other species.
Patients spontaneous dislocation, often with a rapid reduction.
Patients of this type are generally small.
Type VII the form periodontitis is rare and is inherited as an autosomal dominant.
Patients of this type have a dental examination with periodontal gum.
Sagging skin, joint and hyperextensibility bruisability vary.
Gingival resorption and loss of permanent teeth when the patient at the age of 30 years is common.
IX or X-linked cutis laxa type is rare, and a structure in X-linked recessive.
Patients with type IX bilateral bony features on the back.
Rarely the skin and joints are affected.
Chronic diarrhea and outcome of orthostatic hypotension are unique in this group.
The scars are usually visible, because the treatment is poor.
Patients of this type have a defect in intracellular copper-dependent enzymes, similar to that of patients with Menkes syndrome.
Type X (fibronectin deficiency) and type XI (benign hypermobility syndrome) is a rare form of Ehlers-Danlos syndrome. Some suggest that these species are so similar that you are better classified as a category 2
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